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Association of Bacillus Calmette-Guerin (BCG) vaccination with reduced risk of PFAPA: nationwide matched case-control study using electronic health records

2026-01-05 epidemiology Title + abstract only
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ObjectivesPeriodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome is the most common autoinflammatory disorder of childhood, characterized by recurrent febrile episodes driven by dysregulated innate immune activation. Although genetic susceptibility contributes to disease risk, environmental modifiers remain poorly defined. Vaccinations may induce long-lasting modulation of innate immune responses and influence PFAPA incidence. We aimed to assess whether childhoo...

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