How well does spirometry capture the symptom range in primary ciliary dyskinesia? -- a cross-sectional national study

2025-08-27 respiratory medicine Title + abstract only

Show abstract

IntroductionPatients with primary ciliary dyskinesia (PCD) present a variety of respiratory symptoms. Spirometry, particularly forced expiratory volume in 1 s (FEV1), is the most commonly used outcome measure in clinical follow-up, however, it is not known how well it captures the range of respiratory symptoms experienced by patients. MethodsWe sent the FOLLOW-PCD questionnaire to all patients [≥]14 years and parents of children, registered in the Swiss PCD Registry, asking about upper and l...