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Incidence and predictors of pulmonary exacerbations in primary ciliary dyskinesia: an international prospective cohort study

2025-01-14 epidemiology Title + abstract only
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IntroductionPulmonary exacerbations contribute to disease progression in chronic lung diseases. In a large prospective cohort study, we studied the incidence and predictors of pulmonary exacerbations among persons with primary ciliary dyskinesia (PCD), which can inform follow-up care. We also assessed healthcare use, changes in management, and pathogens during exacerbations. MethodsParticipants in the Living with PCD study reported increased respiratory symptoms in the past seven days, indicati...

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